Extranodal NK/T cell lymphoma, nasal type

Extranodal NK/T cell lymphoma, nasal type
Updated: 08/30/2024
© Jun Wang, MD, PhD

General features
  • Rare, extranodal lymphoma
  • Highly aggressive
  • Express CD56 if NK cells
  • CD56 positive in some cases of T cell lineage
  • Positive for EBV in all cases
Clinical presentations
  • Most common site: Upper aerodigestive tract
  • Rapidly growing mass
  • Vascular damage and destruction
  • Prominent necrosis
Key pathogenesis
  • EB Virus



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Contents

Pathology notes Jun Wang, MD, PhD 1. General information Frequently discussed syndromes Terms of dermatology Terms of hematology 2. Primary immunodeficiency disorders 3. Hemodynamic abnormalities Shock Thrombosis and embolism Bleeding disorders 4.  Benign blood cell disorders Anemia Benign white cell disorders 5. Hematopoietic neoplasms Lymphoid neoplasms Myeloid neoplasms Histiocytic neoplasms: Langerhans cell histiocytosis 6. Cardiovascular system Pulmonary hypertension Cardiovascular system tumors 7. Respiratory tract tumors 8. Gastrointestinal tract Congenital disorders Infectious gastroenteritis Oral cavity Esophagus Stomach Intestinal tumors Salivary glands Exocrine pancreas and gallbladder 9. Urinary system Kidney masses Lower urinary tract 10. Male reproductive system 11. Female genital tract 12. Breast 13. Endocrine organs Pituitary gland Adrenal gland Thyroid gland Parathyroid gland Endocrine pancreas...
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Anemia

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Lymphoid neoplasms

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