Congenital diaphragmatic hernia

Congenital diaphragmatic hernia
Updated: 02/22/2019
© Jun Wang, MD, PhD

General features
  • Developmental defect of diaphragm
  • More common in left
  • Abdominal organs herniated into chest
Basic types
  • Paravertebral/posterolateral type (Bochdalek type): Most common
  • Parasternal type (in the foramen of Morgagni)
  • Hiatal hernia
Clinical presentations
  • Respiratory distress due to lung compression and hypoplasia
Prenatal diagnosis
  • Image studies
Radiologic findings
  • Abdominal organ (most commonly intestine) in chest
Pathological findings
  • Diaphragmatic defects
  • Abdominal organ (most commonly intestine) in chest
Diagnosis
  • Suspected in any term infants with respiratory distress
  • Radiologic studies
Treatment
  • Stabilization of oxygenation, etc, followed by surgery


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