Esophageal atresia

Esophageal atresia
Updated: 02/20/2019
© Jun Wang, MD, PhD

General features
  • Group of congenital anomalies of non-patent esophagus
  • With or without fistulae with trachea
  • Associated with congenital heart disease, neurologic disease, GI or GU malformations and single umbilical artery
Etiology
  • Unknown
Clinical presentations
  • Polyhydramnios of mother, excess oral secretion, choke during suckling
  • Failure of inserting NG tube
Key pathological features
  • Proximal blind pouch connected to pharynx
  • Distal pouch leading to stomach
Diagnosis
  • Clinical symptoms, radiologic studies
Treatment
  • Surgery



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Contents

Pathology notes Jun Wang, MD, PhD 1. General information Frequently discussed syndromes Terms of dermatology Terms of hematology 2. Primary immunodeficiency disorders 3. Hemodynamic abnormalities Shock Thrombosis and embolism Bleeding disorders 4.  Benign blood cell disorders Anemia Benign white cell disorders 5. Hematopoietic neoplasms Lymphoid neoplasms Myeloid neoplasms Histiocytic neoplasms: Langerhans cell histiocytosis 6. Cardiovascular system Pulmonary hypertension Cardiovascular system tumors 7. Respiratory tract tumors 8. Gastrointestinal tract Congenital disorders Infectious gastroenteritis Oral cavity Esophagus Stomach Intestinal tumors Salivary glands Exocrine pancreas and gallbladder 9. Urinary system Kidney masses Lower urinary tract 10. Male reproductive system 11. Female genital tract 12. Breast 13. Endocrine organs Pituitary gland Adrenal gland Thyroid gland Parathyroid gland Endocrine pancreas M
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Anemia

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Lymphoid neoplasms

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