Cylindroma

Cylindroma 

Updated: 02/24/2020

© Jun Wang, MD, PhD

General features
  • Solitary, small, slow growing
  • Predominantly in head and neck
  • More common in > 40, women
  • Familial form (turban tumor syndrome, Brooke-Spiegler syndrome)
Autosomal dominant
Multiple tumors
Children/teenagers
May involve trunk and extremities, or in association with other adnexal tumors
Mutations in CYLD gene at chromosome 16q12-13
Rarely undergoes malignant transformation
Clinical features
Pathological features
Management
  • Excision
  • Follow up for patients with multiple tumors, since recurrence likely



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Contents

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