Megaloblastic anemia

Megaloblastic anemia

Updated: 7/17/2024

© Jun Wang, MD, PhD

 

General features

  • Heterogeneous group
  • Macrocytic anemia with an arrest in nuclear maturation
  • Characterized by presence of megaloblasts: large nucleated RBC precursors

Etiology

  • Vitamin B12 deficiency

o   Gastric abnormalities

§  Gastrectomy/bariatric surgery

§  Gastritis, include autoimmune gastritis

o   Small bowel disease

§  Malabsorption, Celiac disease, inflammatory bowel disease

§  Ileal resection or bypass, blind loop

§  Bacterial overgrowth, fish tapeworm

o   Pancreatitis: Pancreatic insufficiency

o   Diet: Breastfed infant of a VB12 deficiet mother, vegan diet, lack animal protein during pregnancy/lactation, etc

o   Medication impairing VB12 absorption or metabolism

o   Inherited transcobalamin II deficiency

  • Folate deficiency

o   Nutritional deficiency

§  Inadequate dietary intake

§  Chronic excessive alcohol use

§  Consumption of overcooked foods

§  Reduced intake of green leafy vegetables

o   Malabsorption disorders: Celiac disease, short bowel syndrome, etc

o   Drugs: methotrexate, trimethoprim, ethanol, phenytoin

o   Increased requirements

§  Pregnancy, lactation

§  Chronic hemolysis

§  Exfoliative dermatitis or severe eczema

§  Other conditions with high cellular turnover

  • Copper deficiency
  • Medications that interfere with DNA synthesis, e.g. chemotherapy (5FU), antiretroviral (AZT), antimetabolite (MTX), etc

Pernicious anemia

  • VB12 deficiency secondary to autoimmune gastritis
  • Resulted from impaired intrinsic factor production by parietal cells, or abnormal intrinsic factor function
  • Three types of autoantibodies

o   Type I: blocks binding of B12 to IF (seen in 75%)

o   Type II: prevent binding of IF-B12 complex ileal receptor

o   Type III: against parietal cell proton pump, causing damage of parietal cells

  • Patients may have history of other autoimmune diseases,
  • Risk for gastric adenocarcinoma

Pathogenesis

  • VB12 needed for production of thymidine
  • Folate needed for production of purine base and thymidine
  • Purine and thymidine needed for DNA synthesis


Key clinical findings

  • Common to both B12 and Folate deficiency

o   Megaloblastic anemia

o   Fatigue, weight loss, fever, jaundice, decreased appetite, diarrhea, sore tongue, and fundal hemorrhages in severe cases

  • More commonly vitamin B12 deficiency

o   Densory parasthesias

o   Motor neuropathy

o   Spinal cord demyelination

o   Dementia

  • More commonly pernicious anemia

o   Family or personal history of vitiligo

o   Autoimmune thyroid disease: Hashimoto thyroiditis, Grave disease

o   Other autoinflammatory disease

Key Laboratory and pathological findings

  • CBC

o   Low Hb, reticulocytes

o   High MCV (>100 fl)

o   Elevated RDW

o   Macro-ovalocytosis, hypersegmented neutrophils

o   Mild leukopenia and/or thrombocytopenia

  • Reduce serum VB12 and/or folate
  • VB12 deficiency: Elevated methylmalonic acid [MMA] and homocysteine
  • Folate deficiency: Normal methylmalonic acid [MMA] and elevated homocysteine
  • Autoantibodies to intrinsic factor
  • Bone marrow: usually not indicated, help ruling out Myelodysplastic syndrome (MDS) and assess iron stores

Management

  • Treatment focus on causes
  • Favorable prognosis if the etiology identified and appropriate treatment instituted

 

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