Zollinger-Ellison Syndrome

Zollinger-Ellison Syndrome
Updated: 01/21/2021
© Jun Wang, MD, PhD

General features
  • Gastrinoma
  • Tumor of G-cell (more commonly in pyloric glands, occasionally in pancreas)
  • Functionally active and usually malignant
  • Either sporadic non-familial with ZES (more common) or familial with ZES in the setting of MEN1
Clinical presentations
Managements
  • Surgery
  • H2 blockers


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Contents

Pathology notes Jun Wang, MD, PhD 1. General information Frequently discussed syndromes Terms of dermatology Terms of hematology 2. Primary immunodeficiency disorders 3. Hemodynamic abnormalities Shock Thrombosis and embolism Bleeding disorders 4.  Benign blood cell disorders Anemia Benign white cell disorders 5. Hematopoietic neoplasms Lymphoid neoplasms Myeloid neoplasms Histiocytic neoplasms: Langerhans cell histiocytosis 6. Cardiovascular system Pulmonary hypertension Cardiovascular system tumors 7. Respiratory tract tumors 8. Gastrointestinal tract Congenital disorders Infectious gastroenteritis Oral cavity Esophagus Stomach Intestinal tumors Salivary glands Exocrine pancreas and gallbladder 9. Urinary system Kidney masses Lower urinary tract 10. Male reproductive system 11. Female genital tract 12. Breast 13. Endocrine organs Pituitary gland Adrenal gland Thyroid gland Parathyroid gland Endocrine pancreas...
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Anemia

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Lymphoid neoplasms

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